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Gene set: HUMAN_MITODB_6_2002 (C2:EXCU:0048)
Standard nameHUMAN_MITODB_6_2002
Systematic nameC2:EXCU:0048
Brief descriptionMitochondrial genes
CategoryC2: Curated
Sub-categoryEXCU: Expert curation
Full description or Abstract
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Publication URLna
External linksna
Keywords & MeSH headingsna
OrganismHuman
Contributed byVamsi Mootha
Source platformGene_Symbol
Downloadgrp|xml|map
Genes

428 genes, 428 accessions (Toggle view)

GeneTitleLinks
HCLS1hematopoietic cell-specific Lyn substrate 1Source|GeneCards
BZRPbenzodiazapine receptor (peripheral)Source|GeneCards
FIBPfibroblast growth factor (acidic) intracellular binding proteinSource|GeneCards
ATPIF1ATPase inhibitory factor 1Source|GeneCards
MRPS10mitochondrial ribosomal protein S10Source|GeneCards
UQCRC2ubiquinol-cytochrome c reductase core protein IISource|GeneCards
SLC25A11solute carrier family 25 (mitochondrial carrier; oxoglutarate carrier), member 11Source|GeneCards
ACADSacyl-Coenzyme A dehydrogenase, C-2 to C-3 short chainSource|GeneCards
DLDx)Source|GeneCards
SHMT1serine hydroxymethyltransferase 1 (soluble)Source|GeneCards
PDK1pyruvate dehydrogenase kinase, isoenzyme 1Source|GeneCards
NGFRAP1nerve growth factor receptor (TNFRSF16) associated protein 1Source|GeneCards
MRPS33mitochondrial ribosomal protein S33Source|GeneCards
SOD2superoxide dismutase 2, mitochondrialSource|GeneCards
AK3Adenylate kinase 3-like 1Source|GeneCards
GPX4glutathione peroxidase 4 (phospholipid hydroperoxidase)Source|GeneCards
AKAP1A kinase (PRKA) anchor protein 1Source|GeneCards
SLC25A15solute carrier family 25 (mitochondrial carrier; ornithine transporter) member 15Source|GeneCards
BCL2L1BCL2-like 1Source|GeneCards
CRY1cryptochrome 1 (photolyase-like)Source|GeneCards
TXNthioredoxinSource|GeneCards
DIA1diaphorase (NADH) (cytochrome b-5 reductase)Source|GeneCards
DUTdUTP pyrophosphataseSource|GeneCards
ZNF183zinc finger protein 183 (RING finger, C3HC4 type)Source|GeneCards
FRAP1FK506 binding protein 12-rapamycin associated protein 1Source|GeneCards
GATMglycine amidinotransferase (L-arginine:glycine amidinotransferase)Source|GeneCards
MRPS18Amitochondrial ribosomal protein S18ASource|GeneCards
PRSS15protease, serine, 15Source|GeneCards
TOMM34translocase of outer mitochondrial membrane 34Source|GeneCards
NDUFA9NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 9, 39kDaSource|GeneCards
PDK3pyruvate dehydrogenase kinase, isoenzyme 3Source|GeneCards
ATP7BATPase, Cu++ transporting, beta polypeptide (Wilson disease)Source|GeneCards
ACADSBacyl-Coenzyme A dehydrogenase, short/branched chainSource|GeneCards
HSPE1heat shock 10kDa protein 1 (chaperonin 10)Source|GeneCards
ACAA2acetyl-Coenzyme A acyltransferase 2 (mitochondrial 3-oxoacyl-Coenzyme A thiolase)Source|GeneCards
SUCLA2succinate-CoA ligase, ADP-forming, beta subunitSource|GeneCards
ATP5HATP synthase, H+ transporting, mitochondrial F0 complex, subunit dSource|GeneCards
MRPS30mitochondrial ribosomal protein S30Source|GeneCards
TIMM10translocase of inner mitochondrial membrane 10 homolog (yeast)Source|GeneCards
CScitrate synthaseSource|GeneCards
SLC25A13solute carrier family 25, member 13 (citrin)Source|GeneCards
CYP11B1cytochrome P450, family 11, subfamily B, polypeptide 1Source|GeneCards
BDH3-hydroxybutyrate dehydrogenase (heart, mitochondrial)Source|GeneCards
ACAD8acyl-Coenzyme A dehydrogenase family, member 8Source|GeneCards
TK1thymidine kinase 1, solubleSource|GeneCards
COX11COX11 homolog, cytochrome c oxidase assembly protein (yeast)Source|GeneCards
BNIP3LBCL2/adenovirus E1B 19kDa interacting protein 3-likeSource|GeneCards
APAF1apoptotic protease activating factorSource|GeneCards
DNASE2deoxyribonuclease II, lysosomalSource|GeneCards
TUFMTu translation elongation factor, mitochondrialSource|GeneCards
MRPS16mitochondrial ribosomal protein S16Source|GeneCards
CA5Bcarbonic anhydrase VB, mitochondrialSource|GeneCards
HADHAhydroxyacyl-Coenzyme A dehydrogenase/3-ketoacyl-Coenzyme A thiolase/enoyl-Coenzyme A hydratase (trifunctional protein), alpha subunitSource|GeneCards
MRPS28mitochondrial ribosomal protein S28Source|GeneCards
SLC25A21solute carrier family 25 (mitochondrial oxodicarboxylate carrier), member 21Source|GeneCards
MRPS35mitochondrial ribosomal protein S35Source|GeneCards
RPL3ribosomal protein L3Source|GeneCards
SSBP1single-stranded DNA binding protein 1Source|GeneCards
NDUFAB1NADH dehydrogenase (ubiquinone) 1, alpha/beta subcomplex, 1, 8kDaSource|GeneCards
COX15COX15 homolog, cytochrome c oxidase assembly protein (yeast)Source|GeneCards
NDUFB7NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 7, 18kDaSource|GeneCards
UQCRBubiquinol-cytochrome c reductase binding proteinSource|GeneCards
HADHSCL-3-hydroxyacyl-Coenzyme A dehydrogenase, short chainSource|GeneCards
BCS1LBCS1-like (yeast)Source|GeneCards
CYB5cytochrome b-5Source|GeneCards
MRPL11mitochondrial ribosomal protein L11Source|GeneCards
CYCScytochrome c, somaticSource|GeneCards
AFG3L2AFG3 ATPase family gene 3-like 2 (yeast)Source|GeneCards
ATP5F1ATP synthase, H+ transporting, mitochondrial F0 complex, subunit b, isoform 1Source|GeneCards
WARS2tryptophanyl tRNA synthetase 2 (mitochondrial)Source|GeneCards
TFB1Mtranscription factor B1, mitochondrialSource|GeneCards
STARD3START domain containing 3Source|GeneCards
TOMM20translocase of outer mitochondrial membrane 20 homolog (yeast)Source|GeneCards
CLPPClpP caseinolytic protease, ATP-dependent, proteolytic subunit homolog (E. coli)Source|GeneCards
SLC25A17solute carrier family 25 (mitochondrial carrier; peroxisomal membrane protein, 34kDa), member 17Source|GeneCards
MCCC1methylcrotonoyl-Coenzyme A carboxylase 1 (alpha)Source|GeneCards
NDUFB5NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 5, 16kDaSource|GeneCards
NR3C1nuclear receptor subfamily 3, group C, member 1 (glucocorticoid receptor)Source|GeneCards
NDUFS1NADH dehydrogenase (ubiquinone) Fe-S protein 1, 75kDa (NADH-coenzyme Q reductase)Source|GeneCards
HSD3B2hydroxy-delta-5-steroid dehydrogenase, 3 beta- and steroid delta-isomerase 2Source|GeneCards
SLC25A5solute carrier family 25 (mitochondrial carrier; adenine nucleotide translocator), member 5Source|GeneCards
MRPL15mitochondrial ribosomal protein L15Source|GeneCards
UQCRHubiquinol-cytochrome c reductase hinge proteinSource|GeneCards
NDUFB3NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 3, 12kDaSource|GeneCards
POPDC2popeye domain containing 2Source|GeneCards
OGG18-oxoguanine DNA glycosylaseSource|GeneCards
MRPL13mitochondrial ribosomal protein L13Source|GeneCards
NDUFB1NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 1, 7kDaSource|GeneCards
SPG7spastic paraplegia 7, paraplegin (pure and complicated autosomal recessive)Source|GeneCards
COX7A2cytochrome c oxidase subunit VIIa polypeptide 2 (liver)Source|GeneCards
TIMM9translocase of inner mitochondrial membrane 9 homolog (yeast)Source|GeneCards
ECHS1enoyl Coenzyme A hydratase, short chain, 1, mitochondrialSource|GeneCards
GSRglutathione reductaseSource|GeneCards
HMGCL3-hydroxymethyl-3-methylglutaryl-Coenzyme A lyase (hydroxymethylglutaricaciduria)Source|GeneCards
MRPL19mitochondrial ribosomal protein L19Source|GeneCards
RPLP2ribosomal protein, large P2Source|GeneCards
VDAC3voltage-dependent anion channel 3Source|GeneCards
MRPL49mitochondrial ribosomal protein L49Source|GeneCards
PCpyruvate carboxylaseSource|GeneCards
MRPS31mitochondrial ribosomal protein S31Source|GeneCards
PTPRAprotein tyrosine phosphatase, receptor type, ASource|GeneCards
NDUFS2NADH dehydrogenase (ubiquinone) Fe-S protein 2, 49kDa (NADH-coenzyme Q reductase)Source|GeneCards
DCIdodecenoyl-Coenzyme A delta isomerase (3,2 trans-enoyl-Coenzyme A isomerase)Source|GeneCards
OKL38pregnancy-induced growth inhibitorSource|GeneCards
MRPS15mitochondrial ribosomal protein S15Source|GeneCards
SARDHsarcosine dehydrogenaseSource|GeneCards
ETFDHelectron-transferring-flavoprotein dehydrogenaseSource|GeneCards
NDUFB8NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 8, 19kDaSource|GeneCards
UQCRFS1ubiquinol-cytochrome c reductase, Rieske iron-sulfur polypeptide 1Source|GeneCards
MTHFD2methylene tetrahydrofolate dehydrogenase (NAD+ dependent), methenyltetrahydrofolate cyclohydrolaseSource|GeneCards
PDHA1pyruvate dehydrogenase (lipoamide) alpha 1Source|GeneCards
ATP5JATP synthase, H+ transporting, mitochondrial F0 complex, subunit F6Source|GeneCards
LARS2leucyl-tRNA synthetase 2, mitochondrialSource|GeneCards
ABCB6ATP-binding cassette, sub-family B (MDR/TAP), member 6Source|GeneCards
GALR3galanin receptor 3Source|GeneCards
CPT1Acarnitine palmitoyltransferase 1A (liver)Source|GeneCards
COX5Acytochrome c oxidase subunit VaSource|GeneCards
HSD3B1hydroxy-delta-5-steroid dehydrogenase, 3 beta- and steroid delta-isomerase 1Source|GeneCards
BCKDKbranched chain alpha-ketoacid dehydrogenase kinaseSource|GeneCards
TSTthiosulfate sulfurtransferase (rhodanese)Source|GeneCards
SUPV3L1suppressor of var1, 3-like 1 (S. cerevisiae)Source|GeneCards
NDUFS8NADH dehydrogenase (ubiquinone) Fe-S protein 8, 23kDa (NADH-coenzyme Q reductase)Source|GeneCards
MUTmethylmalonyl Coenzyme A mutaseSource|GeneCards
ATP5G3ATP synthase, H+ transporting, mitochondrial F0 complex, subunit c (subunit 9) isoform 3Source|GeneCards
FPGSfolylpolyglutamate synthaseSource|GeneCards
UCP2uncoupling protein 2 (mitochondrial, proton carrier)Source|GeneCards
MRPS18Cmitochondrial ribosomal protein S18CSource|GeneCards
BIDBH3 interacting domain death agonistSource|GeneCards
CPOCarboxypeptidase OSource|GeneCards
MTCH2mitochondrial carrier homolog 2 (C. elegans)Source|GeneCards
CYB5-Mcytochrome b5 outer mitochondrial membrane precursorSource|GeneCards
GOT2glutamic-oxaloacetic transaminase 2, mitochondrial (aspartate aminotransferase 2)Source|GeneCards
BNIP3BCL2/adenovirus E1B 19kDa interacting protein 3Source|GeneCards
GCDHglutaryl-Coenzyme A dehydrogenaseSource|GeneCards
NDUFS4NADH dehydrogenase (ubiquinone) Fe-S protein 4, 18kDa (NADH-coenzyme Q reductase)Source|GeneCards
RPS3Aribosomal protein S3ASource|GeneCards
COX4I1cytochrome c oxidase subunit IV isoform 1Source|GeneCards
SCP2sterol carrier protein 2Source|GeneCards
ATP5LATP synthase, H+ transporting, mitochondrial F0 complex, subunit gSource|GeneCards
MRPL35mitochondrial ribosomal protein L35Source|GeneCards
CASP8caspase 8, apoptosis-related cysteine proteaseSource|GeneCards
COX7Ccytochrome c oxidase subunit VIIcSource|GeneCards
COX6A1cytochrome c oxidase subunit VIa polypeptide 1Source|GeneCards
CNOT7CCR4-NOT transcription complex, subunit 7Source|GeneCards
GRID2glutamate receptor, ionotropic, delta 2Source|GeneCards
TOMM70Atranslocase of outer mitochondrial membrane 70 homolog A (yeast)Source|GeneCards
MRPL2Mitochondrial ribosomal protein L2Source|GeneCards
GCKglucokinase (hexokinase 4, maturity onset diabetes of the young 2)Source|GeneCards
MDH2malate dehydrogenase 2, NAD (mitochondrial)Source|GeneCards
ABCB8ATP-binding cassette, sub-family B (MDR/TAP), member 8Source|GeneCards
TIMM44translocase of inner mitochondrial membrane 44 homolog (yeast)Source|GeneCards
NBS1NibrinSource|GeneCards
IDH3Bisocitrate dehydrogenase 3 (NAD+) betaSource|GeneCards
COX10COX10 homolog, cytochrome c oxidase assembly protein, heme A: farnesyltransferase (yeast)Source|GeneCards
MRPL4mitochondrial ribosomal protein L4Source|GeneCards
MRP63mitochondrial ribosomal protein 63Source|GeneCards
GCATglycine C-acetyltransferase (2-amino-3-ketobutyrate coenzyme A ligase)Source|GeneCards
ODC1ornithine decarboxylase 1Source|GeneCards
ATP5J2ATP synthase, H+ transporting, mitochondrial F0 complex, subunit f, isoform 2Source|GeneCards
TIMM8Atranslocase of inner mitochondrial membrane 8 homolog A (yeast)Source|GeneCards
NDUFC2NADH dehydrogenase (ubiquinone) 1, subcomplex unknown, 2, 14.5kDaSource|GeneCards
CYP11A1cytochrome P450, family 11, subfamily A, polypeptide 1Source|GeneCards
TIMM17Atranslocase of inner mitochondrial membrane 17 homolog A (yeast)Source|GeneCards
PCCBpropionyl Coenzyme A carboxylase, beta polypeptideSource|GeneCards
HSPA9Bheat shock 70kDa protein 9B (mortalin-2)Source|GeneCards
ARG2arginase, type IISource|GeneCards
MBD3methyl-CpG binding domain protein 3Source|GeneCards
TRAP1TNF receptor-associated protein 1Source|GeneCards
FHfumarate hydrataseSource|GeneCards
TOMM40translocase of outer mitochondrial membrane 40 homolog (yeast)Source|GeneCards
CKMT1creatine kinase, mitochondrial 1 (ubiquitous)Source|GeneCards
NDUFA6NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 6, 14kDaSource|GeneCards
HMGCS23-hydroxy-3-methylglutaryl-Coenzyme A synthase 2 (mitochondrial)Source|GeneCards
BCKDHAbranched chain keto acid dehydrogenase E1, alpha polypeptide (maple syrup urine disease)Source|GeneCards
PRDX3peroxiredoxin 3Source|GeneCards
NFKBIL2nuclear factor of kappa light polypeptide gene enhancer in B-cells inhibitor-like 2Source|GeneCards
SUCLG1succinate-CoA ligase, GDP-forming, alpha subunitSource|GeneCards
ACADMacyl-Coenzyme A dehydrogenase, C-4 to C-12 straight chainSource|GeneCards
IVDisovaleryl Coenzyme A dehydrogenaseSource|GeneCards
ETFAelectron-transfer-flavoprotein, alpha polypeptide (glutaric aciduria II)Source|GeneCards
MRPL33mitochondrial ribosomal protein L33Source|GeneCards
MTRF1mitochondrial translational release factor 1Source|GeneCards
ABAT4-aminobutyrate aminotransferaseSource|GeneCards
MAOAmonoamine oxidase ASource|GeneCards
SDHDsuccinate dehydrogenase complex, subunit D, integral membrane proteinSource|GeneCards
IMMTinner membrane protein, mitochondrial (mitofilin)Source|GeneCards
TFAMtranscription factor A, mitochondrialSource|GeneCards
TATtyrosine aminotransferaseSource|GeneCards
C2ORF3chromosome 2 open reading frame 3Source|GeneCards
BLVRAbiliverdin reductase ASource|GeneCards
MRPL42mitochondrial ribosomal protein L42Source|GeneCards
SLC25A3solute carrier family 25 (mitochondrial carrier; phosphate carrier), member 3Source|GeneCards
NDUFA8NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 8, 19kDaSource|GeneCards
AKAP10A kinase (PRKA) anchor protein 10Source|GeneCards
MRPS7mitochondrial ribosomal protein S7Source|GeneCards
SDHBsuccinate dehydrogenase complex, subunit B, iron sulfur (Ip)Source|GeneCards
OATornithine aminotransferase (gyrate atrophy)Source|GeneCards
MFN2mitofusin 2Source|GeneCards
AMTaminomethyltransferase (glycine cleavage system protein T)Source|GeneCards
TIMM23translocase of inner mitochondrial membrane 23 homolog (yeast)Source|GeneCards
HSPA1Aheat shock 70kDa protein 1ASource|GeneCards
ACADVLacyl-Coenzyme A dehydrogenase, very long chainSource|GeneCards
GLUD1glutamate dehydrogenase 1Source|GeneCards
CYBBcytochrome b-245, beta polypeptide (chronic granulomatous disease)Source|GeneCards
NRF1nuclear respiratory factor 1Source|GeneCards
ATP5G1ATP synthase, H+ transporting, mitochondrial F0 complex, subunit c (subunit 9), isoform 1Source|GeneCards
NDUFA4NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 4, 9kDaSource|GeneCards
SLC25A1solute carrier family 25 (mitochondrial carrier; citrate transporter), member 1Source|GeneCards
FDXRferredoxin reductaseSource|GeneCards
GPTglutamic-pyruvate transaminase (alanine aminotransferase)Source|GeneCards
STARsteroidogenic acute regulatorSource|GeneCards
MRPL39mitochondrial ribosomal protein L39Source|GeneCards
TXNRD2thioredoxin reductase 2Source|GeneCards
OPA1optic atrophy 1 (autosomal dominant)Source|GeneCards
NDUFA10NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 10, 42kDaSource|GeneCards
TK2thymidine kinase 2, mitochondrialSource|GeneCards
MRPL48mitochondrial ribosomal protein L48Source|GeneCards
MRPS27mitochondrial ribosomal protein S27Source|GeneCards
ZNF11Bzinc finger protein 11b (KOX 2)Source|GeneCards
PPM2Cprotein phosphatase 2C, magnesium-dependent, catalytic subunitSource|GeneCards
HTATSF1HIV TAT specific factor 1Source|GeneCards
HCCSholocytochrome c synthase (cytochrome c heme-lyase)Source|GeneCards
ATP5C1ATP synthase, H+ transporting, mitochondrial F1 complex, gamma polypeptide 1Source|GeneCards
HK1hexokinase 1Source|GeneCards
ALDH2aldehyde dehydrogenase 2 family (mitochondrial)Source|GeneCards
MTERFtranscription termination factor, mitochondrialSource|GeneCards
MRPS17mitochondrial ribosomal protein S17Source|GeneCards
CKAP1cytoskeleton associated protein 1Source|GeneCards
C10ORF28chromosome 10 open reading frame 28Source|GeneCards
BAK1BCL2-antagonist/killer 1Source|GeneCards
SLC9A6solute carrier family 9 (sodium/hydrogen exchanger), isoform 6Source|GeneCards
UCP3uncoupling protein 3 (mitochondrial, proton carrier)Source|GeneCards
SLC25A10solute carrier family 25 (mitochondrial carrier; dicarboxylate transporter), member 10Source|GeneCards
MPOmyeloperoxidaseSource|GeneCards
MUTYHmutY homolog (E. coli)Source|GeneCards
NDUFB2NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 2, 8kDaSource|GeneCards
POLGpolymerase (DNA directed), gammaSource|GeneCards
COX7A2Lcytochrome c oxidase subunit VIIa polypeptide 2 likeSource|GeneCards
ABCF2ATP-binding cassette, sub-family F (GCN20), member 2Source|GeneCards
CYP11B2cytochrome P450, family 11, subfamily B, polypeptide 2Source|GeneCards
MTIF2mitochondrial translational initiation factor 2Source|GeneCards
GLYATglycine-N-acyltransferaseSource|GeneCards
MRPS18Bmitochondrial ribosomal protein S18BSource|GeneCards
COX6Ccytochrome c oxidase subunit VIcSource|GeneCards
EFG1mitochondrial elongation factor G1Source|GeneCards
SLC25A14solute carrier family 25 (mitochondrial carrier, brain), member 14Source|GeneCards
ACAT1Acetyl-Coenzyme A acetyltransferase 1 (acetoacetyl Coenzyme A thiolase)Source|GeneCards
ALAS1aminolevulinate, delta-, synthase 1Source|GeneCards
SLC25A12solute carrier family 25 (mitochondrial carrier, Aralar), member 12Source|GeneCards
CLPXClpX caseinolytic protease X homolog (E. coli)Source|GeneCards
SLC25A20solute carrier family 25 (carnitine/acylcarnitine translocase), member 20Source|GeneCards
OGDHoxoglutarate (alpha-ketoglutarate) dehydrogenase (lipoamide)Source|GeneCards
NNTnicotinamide nucleotide transhydrogenaseSource|GeneCards
TIMM13translocase of inner mitochondrial membrane 13 homolog (yeast)Source|GeneCards
ATP5EATP synthase, H+ transporting, mitochondrial F1 complex, epsilon subunitSource|GeneCards
ME2malic enzyme 2, NAD(+)-dependent, mitochondrialSource|GeneCards
PPIFpeptidylprolyl isomerase F (cyclophilin F)Source|GeneCards
DLATdihydrolipoamide S-acetyltransferase (E2 component of pyruvate dehydrogenase complex)Source|GeneCards
IDH2isocitrate dehydrogenase 2 (NADP+), mitochondrialSource|GeneCards
PDHBpyruvate dehydrogenase (lipoamide) betaSource|GeneCards
BCKDHBbranched chain keto acid dehydrogenase E1, beta polypeptide (maple syrup urine disease)Source|GeneCards
HAX1HS1 binding proteinSource|GeneCards
MRPL12mitochondrial ribosomal protein L12Source|GeneCards
NDUFB6NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 6, 17kDaSource|GeneCards
CYP27B1cytochrome P450, family 27, subfamily B, polypeptide 1Source|GeneCards
DGUOKdeoxyguanosine kinaseSource|GeneCards
NDUFB4NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 4, 15kDaSource|GeneCards
CA5Acarbonic anhydrase VA, mitochondrialSource|GeneCards
BCL2A1BCL2-related protein A1Source|GeneCards
DHODHdihydroorotate dehydrogenaseSource|GeneCards
COX5Bcytochrome c oxidase subunit VbSource|GeneCards
ATP5BATP synthase, H+ transporting, mitochondrial F1 complex, beta polypeptideSource|GeneCards
MRPS34mitochondrial ribosomal protein S34Source|GeneCards
BC002942hypothetical protein BC002942Source|GeneCards
GLSglutaminaseSource|GeneCards
MPSTmercaptopyruvate sulfurtransferaseSource|GeneCards
MRPL46mitochondrial ribosomal protein L46Source|GeneCards
BCL2L11BCL2-like 11 (apoptosis facilitator)Source|GeneCards
MRPL18mitochondrial ribosomal protein L18Source|GeneCards
HADHBhydroxyacyl-Coenzyme A dehydrogenase/3-ketoacyl-Coenzyme A thiolase/enoyl-Coenzyme A hydratase (trifunctional protein), beta subunitSource|GeneCards
DKFZP586D0919hepatocellularcarcinoma-associated antigen HCA557aSource|GeneCards
PMPCBpeptidase (mitochondrial processing) betaSource|GeneCards
SHMT2serine hydroxymethyltransferase 2 (mitochondrial)Source|GeneCards
SLC25A16solute carrier family 25 (mitochondrial carrier; Graves disease autoantigen), member 16Source|GeneCards
MRPL20mitochondrial ribosomal protein L20Source|GeneCards
BAXBCL2-associated X proteinSource|GeneCards
NDUFS6NADH dehydrogenase (ubiquinone) Fe-S protein 6, 13kDa (NADH-coenzyme Q reductase)Source|GeneCards
OXA1Loxidase (cytochrome c) assembly 1-likeSource|GeneCards
ALDH4A1aldehyde dehydrogenase 4 family, member A1Source|GeneCards
SURF1surfeit 1Source|GeneCards
VDAC2voltage-dependent anion channel 2Source|GeneCards
MRPL44mitochondrial ribosomal protein L44Source|GeneCards
MRPS11mitochondrial ribosomal protein S11Source|GeneCards
POLRMTpolymerase (RNA) mitochondrial (DNA directed)Source|GeneCards
TXN2thioredoxin 2Source|GeneCards
PIN4protein (peptidyl-prolyl cis/trans isomerase) NIMA-interacting, 4 (parvulin)Source|GeneCards
MRPL16mitochondrial ribosomal protein L16Source|GeneCards
NDUFV2NADH dehydrogenase (ubiquinone) flavoprotein 2, 24kDaSource|GeneCards
UQCRC1ubiquinol-cytochrome c reductase core protein ISource|GeneCards
SLC1A3solute carrier family 1 (glial high affinity glutamate transporter), member 3Source|GeneCards
FDX1ferredoxin 1Source|GeneCards
IDH3Gisocitrate dehydrogenase 3 (NAD+) gammaSource|GeneCards
ATP5DATP synthase, H+ transporting, mitochondrial F1 complex, delta subunitSource|GeneCards
AGXTalanine-glyoxylate aminotransferase (oxalosis I; hyperoxaluria I; glycolicaciduria; serine-pyruvate aminotransferase)Source|GeneCards
NME4non-metastatic cells 4, protein expressed inSource|GeneCards
LYPLA2lysophospholipase IISource|GeneCards
CASQ1calsequestrin 1 (fast-twitch, skeletal muscle)Source|GeneCards
ABCB7ATP-binding cassette, sub-family B (MDR/TAP), member 7Source|GeneCards
NDUFA2NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 2, 8kDaSource|GeneCards
HSPD1heat shock 60kDa protein 1 (chaperonin)Source|GeneCards
PCK2phosphoenolpyruvate carboxykinase 2 (mitochondrial)Source|GeneCards
CYP24A1cytochrome P450, family 24, subfamily A, polypeptide 1Source|GeneCards
ATP5SATP synthase, H+ transporting, mitochondrial F0 complex, subunit s (factor B)Source|GeneCards
IVNS1ABPinfluenza virus NS1A binding proteinSource|GeneCards
COX6A2cytochrome c oxidase subunit VIa polypeptide 2Source|GeneCards
ATP5IATP synthase, H+ transporting, mitochondrial F0 complex, subunit eSource|GeneCards
NDUFS7NADH dehydrogenase (ubiquinone) Fe-S protein 7, 20kDa (NADH-coenzyme Q reductase)Source|GeneCards
PDHXpyruvate dehydrogenase complex, component XSource|GeneCards
COX7A1cytochrome c oxidase subunit VIIa polypeptide 1 (muscle)Source|GeneCards
TOMM22translocase of outer mitochondrial membrane 22 homolog (yeast)Source|GeneCards
CPT1Bcarnitine palmitoyltransferase 1B (muscle)Source|GeneCards
BCAT2branched chain aminotransferase 2, mitochondrialSource|GeneCards
PPIDpeptidylprolyl isomerase D (cyclophilin D)Source|GeneCards
MRPL17mitochondrial ribosomal protein L17Source|GeneCards
MRPS14mitochondrial ribosomal protein S14Source|GeneCards
POLG2polymerase (DNA directed), gamma 2, accessory subunitSource|GeneCards
ACADLacyl-Coenzyme A dehydrogenase, long chainSource|GeneCards
ACP6lysophosphatidic acid phosphataseSource|GeneCards
CYP27A1cytochrome P450, family 27, subfamily A, polypeptide 1Source|GeneCards
PET112LPET112-like (yeast)Source|GeneCards
MRPL34mitochondrial ribosomal protein L34Source|GeneCards
DAP3death associated protein 3Source|GeneCards
ENDOGendonuclease GSource|GeneCards
MCFPmitochondrial carrier family proteinSource|GeneCards
SDSserine dehydrataseSource|GeneCards
IDH3Aisocitrate dehydrogenase 3 (NAD+) alphaSource|GeneCards
MTCH1mitochondrial carrier homolog 1 (C. elegans)Source|GeneCards
MTHFD1methylenetetrahydrofolate dehydrogenase (NADP+ dependent), methenyltetrahydrofolate cyclohydrolase, formyltetrahydrofolate synthetaseSource|GeneCards
COQ7coenzyme Q7 homolog, ubiquinone (yeast)Source|GeneCards
UCP1uncoupling protein 1 (mitochondrial, proton carrier)Source|GeneCards
NFS1NFS1 nitrogen fixation 1 (S. cerevisiae)Source|GeneCards
RAF1v-raf-1 murine leukemia viral oncogene homolog 1Source|GeneCards
GOT1glutamic-oxaloacetic transaminase 1, soluble (aspartate aminotransferase 1)Source|GeneCards
CPS1carbamoyl-phosphate synthetase 1, mitochondrialSource|GeneCards
OTCornithine carbamoyltransferaseSource|GeneCards
DNM1Ldynamin 1-likeSource|GeneCards
COX7Bcytochrome c oxidase subunit VIIbSource|GeneCards
PYCR1pyrroline-5-carboxylate reductase 1Source|GeneCards
MLH3mutL homolog 3 (E. coli)Source|GeneCards
NDUFS3NADH dehydrogenase (ubiquinone) Fe-S protein 3, 30kDa (NADH-coenzyme Q reductase)Source|GeneCards
HSPA1Lheat shock 70kDa protein 1-likeSource|GeneCards
AK2adenylate kinase 2Source|GeneCards
PCCApropionyl Coenzyme A carboxylase, alpha polypeptideSource|GeneCards
KIAA0963KIAA0963 proteinSource|GeneCards
DECR12,4-dienoyl CoA reductase 1, mitochondrialSource|GeneCards
TIMM17Btranslocase of inner mitochondrial membrane 17 homolog B (yeast)Source|GeneCards
CPT2carnitine palmitoyltransferase IISource|GeneCards
ME3malic enzyme 3, NADP(+)-dependent, mitochondrialSource|GeneCards
UQCRubiquinol-cytochrome c reductase (6.4kD) subunitSource|GeneCards
NOC4neighbor of COX4Source|GeneCards
OAZINornithine decarboxylase antizyme inhibitorSource|GeneCards
ETFBelectron-transfer-flavoprotein, beta polypeptideSource|GeneCards
ACO2aconitase 2, mitochondrialSource|GeneCards
SLC25A28solute carrier family 25, member 28Source|GeneCards
SLC1A1solute carrier family 1 (neuronal/epithelial high affinity glutamate transporter, system Xag), member 1Source|GeneCards
HLCSholocarboxylase synthetase (biotin-[proprionyl-Coenzyme A-carboxylase (ATP-hydrolysing)] ligase)Source|GeneCards
BCL2B-cell CLL/lymphoma 2Source|GeneCards
MRPS12mitochondrial ribosomal protein S12Source|GeneCards
NDUFC1NADH dehydrogenase (ubiquinone) 1, subcomplex unknown, 1, 6kDaSource|GeneCards
CYC1cytochrome c-1Source|GeneCards
384D8-2hypothetical protein 384D8_6Source|GeneCards
DBTdihydrolipoamide branched chain transacylase (E2 component of branched chain keto acid dehydrogenase complex; maple syrup urine disease)Source|GeneCards
ATP5OATP synthase, H+ transporting, mitochondrial F1 complex, O subunit (oligomycin sensitivity conferring protein)Source|GeneCards
NDUFA5NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 5, 13kDaSource|GeneCards
ATP5G2ATP synthase, H+ transporting, mitochondrial F0 complex, subunit c (subunit 9), isoform 2Source|GeneCards
UROSuroporphyrinogen III synthase (congenital erythropoietic porphyria)Source|GeneCards
FECHferrochelatase (protoporphyria)Source|GeneCards
DIABLOdiablo homolog (Drosophila)Source|GeneCards
CLN3ceroid-lipofuscinosis, neuronal 3, juvenile (Batten, Spielmeyer-Vogt disease)Source|GeneCards
C10ORF6chromosome 10 open reading frame 6Source|GeneCards
GPD2glycerol-3-phosphate dehydrogenase 2 (mitochondrial)Source|GeneCards
MRPS2mitochondrial ribosomal protein S2Source|GeneCards
PDK4pyruvate dehydrogenase kinase, isoenzyme 4Source|GeneCards
NDUFA7NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 7, 14.5kDaSource|GeneCards
MRPS22mitochondrial ribosomal protein S22Source|GeneCards
DLSTdihydrolipoamide S-succinyltransferase (E2 component of 2-oxo-glutarate complex)Source|GeneCards
MAOBmonoamine oxidase BSource|GeneCards
MIPEPmitochondrial intermediate peptidaseSource|GeneCards
NDUFA3NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 3, 9kDaSource|GeneCards
NDUFS5NADH dehydrogenase (ubiquinone) Fe-S protein 5, 15kDa (NADH-coenzyme Q reductase)Source|GeneCards
MRPL22mitochondrial ribosomal protein L22Source|GeneCards
TIMM8Btranslocase of inner mitochondrial membrane 8 homolog B (yeast)Source|GeneCards
TIMM22translocase of inner mitochondrial membrane 22 homolog (yeast)Source|GeneCards
SDHAsuccinate dehydrogenase complex, subunit A, flavoprotein (Fp)Source|GeneCards
GLUD2glutamate dehydrogenase 2Source|GeneCards
BADBCL2-antagonist of cell deathSource|GeneCards
CKMT2creatine kinase, mitochondrial 2 (sarcomeric)Source|GeneCards
PDCD8programmed cell death 8 (apoptosis-inducing factor)Source|GeneCards
SDHCsuccinate dehydrogenase complex, subunit C, integral membrane protein, 15kDaSource|GeneCards
CRATcarnitine acetyltransferaseSource|GeneCards
CYBAcytochrome b-245, alpha polypeptideSource|GeneCards
MRPL9mitochondrial ribosomal protein L9Source|GeneCards
MRPL24mitochondrial ribosomal protein L24Source|GeneCards
PPOXprotoporphyrinogen oxidaseSource|GeneCards
SLC25A4solute carrier family 25 (mitochondrial carrier; adenine nucleotide translocator), member 4Source|GeneCards
AMACRalpha-methylacyl-CoA racemaseSource|GeneCards
MFN1mitofusin 1Source|GeneCards


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