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Gene set: Valine, leucine and isoleucine degradation (C2:PATH:0420)
Standard nameValine, leucine and isoleucine degradation
Systematic nameC2:PATH:0420
Brief descriptionna
CategoryC2: Curated
Sub-categoryPATH: Pathway database
Full description or Abstract
na
Publication URLna
External linksMore details for this gene set:
http://www.genome.jp/kegg/pathway/map/map00280.html
Keywords & MeSH headingsna
OrganismGeneric
Contributed byGenMAPP
Source platformGene_Symbol
Downloadgrp|xml|map
Genes

36 genes, 36 accessions (Toggle view)

GeneTitleLinks
ACADLacyl-Coenzyme A dehydrogenase, long chainSource|GeneCards
HADHBhydroxyacyl-Coenzyme A dehydrogenase/3-ketoacyl-Coenzyme A thiolase/enoyl-Coenzyme A hydratase (trifunctional protein), beta subunitSource|GeneCards
PCCApropionyl Coenzyme A carboxylase, alpha polypeptideSource|GeneCards
MCCC1methylcrotonoyl-Coenzyme A carboxylase 1 (alpha)Source|GeneCards
ALDH3A2aldehyde dehydrogenase 3 family, member A2Source|GeneCards
PCCBpropionyl Coenzyme A carboxylase, beta polypeptideSource|GeneCards
HADHAhydroxyacyl-Coenzyme A dehydrogenase/3-ketoacyl-Coenzyme A thiolase/enoyl-Coenzyme A hydratase (trifunctional protein), alpha subunitSource|GeneCards
BCKDHBbranched chain keto acid dehydrogenase E1, beta polypeptide (maple syrup urine disease)Source|GeneCards
OXCT13-oxoacid CoA transferase 1Source|GeneCards
EHHADHenoyl-Coenzyme A, hydratase/3-hydroxyacyl Coenzyme A dehydrogenaseSource|GeneCards
ALDH1A2aldehyde dehydrogenase 1 family, member A2Source|GeneCards
SDSserine dehydrataseSource|GeneCards
ACAT1Acetyl-Coenzyme A acetyltransferase 1 (acetoacetyl Coenzyme A thiolase)Source|GeneCards
AOX1aldehyde oxidase 1Source|GeneCards
ALDH1B1aldehyde dehydrogenase 1 family, member B1Source|GeneCards
ACADSacyl-Coenzyme A dehydrogenase, C-2 to C-3 short chainSource|GeneCards
ALDH1A3aldehyde dehydrogenase 1 family, member A3Source|GeneCards
BCAT1branched chain aminotransferase 1, cytosolicSource|GeneCards
ACADSBacyl-Coenzyme A dehydrogenase, short/branched chainSource|GeneCards
ACAA2acetyl-Coenzyme A acyltransferase 2 (mitochondrial 3-oxoacyl-Coenzyme A thiolase)Source|GeneCards
ALDH9A1aldehyde dehydrogenase 9 family, member A1Source|GeneCards
BCKDHAbranched chain keto acid dehydrogenase E1, alpha polypeptide (maple syrup urine disease)Source|GeneCards
ALDH2aldehyde dehydrogenase 2 family (mitochondrial)Source|GeneCards
MCCC2methylcrotonoyl-Coenzyme A carboxylase 2 (beta)Source|GeneCards
ALDH6A1aldehyde dehydrogenase 6 family, member A1Source|GeneCards
ACAT2acetyl-Coenzyme A acetyltransferase 2 (acetoacetyl Coenzyme A thiolase)Source|GeneCards
ECHS1enoyl Coenzyme A hydratase, short chain, 1, mitochondrialSource|GeneCards
ACADMacyl-Coenzyme A dehydrogenase, C-4 to C-12 straight chainSource|GeneCards
IVDisovaleryl Coenzyme A dehydrogenaseSource|GeneCards
HMGCL3-hydroxymethyl-3-methylglutaryl-Coenzyme A lyase (hydroxymethylglutaricaciduria)Source|GeneCards
ALDH1A1aldehyde dehydrogenase 1 family, member A1Source|GeneCards
MUTmethylmalonyl Coenzyme A mutaseSource|GeneCards
MCEEmethylmalonyl CoA epimeraseSource|GeneCards
ALDH3A1aldehyde dehydrogenase 3 family, memberA1Source|GeneCards
HIBADH3-hydroxyisobutyrate dehydrogenaseSource|GeneCards
ACAA1acetyl-Coenzyme A acyltransferase 1 (peroxisomal 3-oxoacyl-Coenzyme A thiolase)Source|GeneCards


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